RTIICS cures Bangla girl’s genetic disorder


Kolkata: Rabindranath Tagore International Institute of Cardiac Sciences (RTIICS) achieved a milestone in the treatment of young Rachana (name changed), a 10-year-old girl from Bangladesh born with a rare genetic disorder called, Familial Hypercholesterolemia (FH). This is an inherited condition, in which the level of bad cholesterol in the blood is much higher than normal (total cholesterol more than 600) from birth leading to aggressive and premature cardiovascular disease. High deposition of lipids in the coronary artery had started hampering the nutrition supply to the heart muscles.

The pediatric cardiac team at RTIICS performed a coronary artery bypass surgery (CABG) on the girl to clear the blocks. New vessels were harvested to rectify the myocardial damage (Cardiac Muscle damage). As confirmed by doctors at RTIICS, she is the youngest girl in Eastern India who underwent a CABG as a result of Familial Hypercholesterolemia.

 Assessing the threat to life posed by this medical condition, if not treated, Dr. Mrinalendu Das, Senior Cardiothoracic  Surgeon, RTIICS along with his team of experts that included Dr. Amitabha Chattopadhyay, Consultant Intervention al Pediatric Cardiologist, Dr. Biswajit Bandopadhay, Consultant Pediatric Cardiologist, Dr. Emanuel Rupert, Cardiac Anesthetist & Zonal Clinical Director, Senior Consultant & Head, Dr. Saibal Roy Chowdhury, Senior Consultant, Anaesthesiology & Critical Care, including Dr. Mahua Roy and Dr. Kuntal Bhattacharya and Dr. Lokesh Kukatla decided to perform a Coronary Artery Bypass Grafting on her with three venous grafts.

Commenting on the complexity of the case, Dr. Mrinalendu Das, Senior Cardiothoracic Surgeon, Rabindranath Tagore International Institute of Cardiac Sciences said, “It was necessary for us to harvest new vessels from other parts of the body, considering the whole aorta and internal mammary was diseased. The processes of placing the grafts were extremely challenging since this type of surgeries are usually performed on adults.”